【Objective】To study the dental status，the development of jaw and the size of sella turcica of children with ectoder? mal dysplasia（ED）. 【Methods】Panaramic radiography and lateral cephalograms of six ED individuals（age range of 6 ~ 7 years，five males and one female）were obtained. The dental status was record. 17 measurements about the jaws and the sella turcica were mea? sured and compare them to Chinese children without ED syndrome.【Results】The mean number of missing teeth was 22.3 in perma? nent dentition and 16.2 in primary dentition；The teeth that most likely to absent were permanent lateral incisor，maxillary first premo? lar，maxillary primary lateral incisor and mandibular primary central incisor，and all remaining teeth are in conical shape. Lateral cephalometric measurements showed that all ED subjects had lower ANS-Ptm，which suggested a short maxilla. Low Co-Po，ANB， NA-PA，N-Me，N-ANS and ANS-Me values that were found in all subjects，as well as low SNA，Y-axis，MP-FH，S-Co，and high SNB，NP-FH，NP-FH that were noted in some subjects showed counterclockwise rotation and protrusion of mandible with short? er length in ED subjects. Some subjects had low ANS-Me/N-Me×100% and high N-ANS/N-Me×100%，representing a short facial height. Five cases represented lower length and diameter of sella turcica；two cases showed lower depth of sella turcica，indicating the abnormal development of sella turcica.【Conclusion】The results of this study suggest that the dentition，jaws and sella turcica in ED children differs when compared to individuals without this syndrome.